1
Cardiology section, Department of Medicine, Aga Khan University Hospital, Karachi, Pakistan
Received: 2017-08-07
Revised: 2018-01-01
Accepted: 2018-03-12
Published: 2018-03-29
Budd‑Chiari syndrome (BCS) is a rare clinical disorder which is caused by obstruction of the major hepatic veins or suprahepatic portion of the inferior vena cava. Either thrombosis or a mechanical venous obstruction may be present. BCS has been shown to be associated with a number of diseases including polycythaemia vera, myeloproliferative disorders, malignancy or congenital web of the gastro‑in testinal tract. Right‑sided cardiac tumours, although rarely reported as a cause for BCS, are generally considered as a surgically curable cause for this otherwise potentially lethal clinical condition.
rare disease, cardiac tumour, cardiac magnetic resonance imaging, computed tomography, echocardiography, cardiac surgery