Background: Balloon aortic valvuloplasty (BAV) is a well-established and minimally invasive interventional procedure for relieving congenital aortic stenosis (AS) in neonates. Despite its efficacy in reducing left ventricular outflow obstruction, the risk of post-procedural aortic regurgitation (AR) remains a concern, with literature citing incidence rates between 7% and 27%. Early antenatal detection of severe AS allows appropriate perinatal planning and timely postnatal intervention, which can significantly improve outcomes and reduce complications. Case Report: We present the case of a term male neonate (3.28 kg) born at 38 weeks and 5 days of gestation via elective cesarean section. Fetal echocardiography had revealed severe congenital aortic stenosis with a bicuspid aortic valve. Postnatally, the infant was hemodynamically stable with a grade 3 ejection systolic murmur. Echocardiography confirmed severe valvular AS (AV peak gradient 95 mmHg; mean gradient 50 mmHg) with preserved left ventricular function. On day 17 of life, BAV was performed under general anesthesia using sequential 5 mm and 8 mm Tyshak balloons. Left ventricular pressure decreased from 144 mmHg to 74 mmHg, and post-procedure echocardiography showed a marked reduction in gradient (peak 18 mmHg, mean 9 mmHg) without any aortic regurgitation. A transient femoral artery thrombosis was identified post-procedure and successfully managed with low-dose heparin infusion. The infant was discharged in stable condition the following day.