Arrhythmogenic right ventricular cardiomyopathy (ARVC) is caused by replacement of myocardial cells by lipocytes and fibrocytes. The disease is associated with life-threatening ventricular arrhythmias. Echocardiography is an easily accessible and useful diagnostic tool in these patients We present a case of an ARVC patient with high risk of sudden cardiac death and thrombus formation in the right ventricle. JRCD 2015; 2 (5): 165–168