Isolated non‑compaction cardiomyopathy is a rare congenital developmental disorder, which belongs to the group of unclassified cardiomyopathies by the ESC Position Statement. Typical echocardiographic findings include multiple trabeculations of the left ventricular muscle, separated by deep lacunae which communicate with left ventricular lumen. We present a case of accidentally discovered non‑compaction cardiomyopathy in a 46‑year‑old male, who was initially diagnosed with an acute coronary syndrome. The diagnosis of the left ventricular non‑compaction was confirmed by transthoracic echocardiography and cardiac magnetic resonance. Occupational contribution (lead and zinc exposure and repeated electric shocks) to the onset of the heart failure was additionally evaluated. JRCD 2013; 1 (3): 17–22